Authors

* Professor of Orthopeadic, Department of Orthopedics, Orthopedic Research Center, Shiraz University of Medical Sciences, Shiraz, Iran

Abstract

Abstract
Background Primary Epithelioid Hemangioendothelioma (EHE) of spine is an extremely rare malignant vascular neoplasm with unpredictable outcome. As a malignant tumor, total resection offers the best possible disease -free survival, while the location poses difficult technical problems .
Method: A 38-year-old man with a large tumor of T10 vertebra was investigated, had biopsy-confirmed diagnosis of EHE, and underwent simultaneous anterior and posterior resection and reconstruction with anterior strut grafting and posteriorly instrumented fusion.
Results: The patient has had good a post-operative course with no neurological damage and no recurrence found in the one-year follow-up .
Conclusion: EHE of thoracic spine is a rare finding and a well-planned total surgical excision can produce a good outcome.
 
 

Keywords

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