Spondylectomy of Epithelioid Hemangio-endothelioma of Thoracic Spine and  Technical Resection Issues  (Case Report)

Nouraei, Hormoz; Motalebi, Morad

doi:10.22034/ijos.2021.139490

Spondylectomy of Epithelioid Hemangio-endothelioma of Thoracic Spine and Technical Resection Issues (Case Report)

Authors

Hormoz Nouraei

Morad Motalebi

* Professor of Orthopeadic, Department of Orthopedics, Orthopedic Research Center, Shiraz University of Medical Sciences, Shiraz, Iran

https://doi.org/10.22034/ijos.2021.139490

Abstract

Abstract
Background Primary Epithelioid Hemangioendothelioma (EHE) of spine is an extremely rare malignant vascular neoplasm with unpredictable outcome. As a malignant tumor, total resection offers the best possible disease -free survival, while the location poses difficult technical problems .
Method: A 38-year-old man with a large tumor of T10 vertebra was investigated, had biopsy-confirmed diagnosis of EHE, and underwent simultaneous anterior and posterior resection and reconstruction with anterior strut grafting and posteriorly instrumented fusion.
Results: The patient has had good a post-operative course with no neurological damage and no recurrence found in the one-year follow-up .
Conclusion: EHE of thoracic spine is a rare finding and a well-planned total surgical excision can produce a good outcome.

Keywords

Keywords: Hemangioendothelioma

Thoracic Vertebrae

Vascular Neoplasms

Spine

Spinal fusion

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